Zinner's syndrome: clinical case of a rare pathology
https://doi.org/10.21886/2308-6424-2023-11-3-149-155
Abstract
Zinner’s syndrome is a rare congenital urogenital anomaly characterised by the triad of seminal vesicle cyst, ipsilateral renal aplasia, and seminal duct obstruction. According to the published data, the incidence of seminal vesicle cysts with ipsilateral renal agenesis is 0.0046%, but the true incidence appears to be higher. The article presents a rare clinical case of patient K, 17 years old, followed since birth with a solitary right kidney. The patient was repeatedly examined (ultrasound, cystography, urography, abdominal MRI, pelvic CT). The boy was admitted to our clinic with the diagnosis of "Solitary right kidney" and pelvic cystic formation detected according to the last CT scan. MRI examination of the small pelvis, cystoscopy, diagnostic laparoscopy, puncture of the cystic mass were performed. The diagnosis of "Zinner's syndrome" was made. The size of the cyst did not change during follow-up.
About the Authors
D. A. Dobroserdov
St.Petersburg Children's City Multidisciplinary Clinical Specialised Centre of High Medical Technologies; Mechnikov North-Western State Medical University
Russian Federation
Competing Interests:
Russian Federation
Dmitrii A. Dobroserdov — M.D., Cand.Sc.(Med); Pediatric Urologist and Andrologist, Pediatric Urology and Andrology Division; Assist.Prof., Dept. of Pediatric Surgery
St. Petersburg
Competing Interests:
The authors declare no conflicts of interest.
M. P. Kuchinskii
St.Petersburg Children's City Multidisciplinary Clinical Specialised Centre of High Medical Technologies
Russian Federation
Competing Interests:
Russian Federation
Mikhail P. Kuchinskii — M.D.; Head, Pediatric Urology and Andrology Division
St. Petersburg
Competing Interests:
The authors declare no conflicts of interest.
N. A. Filatova
St.Petersburg Children's City Multidisciplinary Clinical Specialised Centre of High Medical Technologies
Russian Federation
Competing Interests:
Russian Federation
Natalia A. Filatova — Pediatric Urologist and Andrologist, Pediatric Urology and Andrology Division
St. Petersburg
Competing Interests:
The authors declare no conflicts of interest.
L. T. Nalgieva
Mechnikov North-Western State Medical University
Russian Federation
Competing Interests:
Russian Federation
Leila T. Nalgieva — Clinical Resident, Dept. of Pediatric Surgery
St. Petersburg
Competing Interests:
The authors declare no conflicts of interest.
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Review
For citations:
Dobroserdov D.A., Kuchinskii M.P., Filatova N.A., Nalgieva L.T. Zinner's syndrome: clinical case of a rare pathology. Urology Herald. 2023;11(3):149-155. (In Russ.) https://doi.org/10.21886/2308-6424-2023-11-3-149-155
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