Urological anomalies in OHVIRA syndrome (Herlyn-Werner-Wunderlich syndrome)
https://doi.org/10.21886/2308-6424-2022-10-2-109-123
Abstract
We provide a systematic review of articles related to OHVIRA syndrome (Herlyn-Werner-Wunderlich syndrome), found in PubMed/MedLine, Web of Science, Scopus, Scirus, The Cochrane Library and eLIBRARy to show how the urological component of this congenital malformation, previously considered as a concomitant anomaly, has become an important diagnostic marker. Several attempts were made to classify this condition, and they got more complex to include these variants of abnormalities of the kidney and ureter that were found due to advances in imaging technology. As a result, the understanding of the medical community about the OHVIRA syndrome has gradually changed over the past hundred years, and the growing interest of pediatric urologists and surgeons, in turn, has contributed to the early diagnosis of the syndrome and the improvement of examination methods.
About the Authors
K. Lodeikina
Mechnikov North-Western State Medical University; St. Mary Magdalene St. Petersburg Children's City Hospital No. 2
Russian Federation
Russian Federation
Ksenia Lodeikina – M.D.; Postgrad. Student, Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course); Pediatric Urologist and Andrologist
41 Kirochnaya St., St. Petersburg, 191015
47 2nd Ln., Vasileostrovskiy district, St. Petersburg, 199053
I. M. Kagantsov
Mechnikov North-Western State Medical University; Almazov National Medical Research Centre
Russian Federation
Russian Federation
Ilya M. Kagantsov – M.D., Dr.Sci.(Med.); Prof., Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course); Head, Research Laboratory for Surgery of Congenital and Hereditary Pathology
41 Kirochnaya St., St. Petersburg, 191015
2 Akkuratova St., St. Petersburg, 197341
S. A. Karavaeva
Mechnikov North-Western State Medical University
Russian Federation
Russian Federation
Svetlana A. Karavaeva – M.D., Dr.Sci.(Med.), Full Prof.; Head, Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course)
41 Kirochnaya St., St. Petersburg, 191015
N. A. Kokhreidze
Almazov National Medical Research Centre
Russian Federation
Russian Federation
Nadezda A. Kokhreidze – M.D., Dr.Sci.(Med.); Assoc. Prof., Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course); Head, Division of Adolescent Gynecology
2 Akkuratova St., St. Petersburg, 197341
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Review
For citations:
Lodeikina K., Kagantsov I.M., Karavaeva S.A., Kokhreidze N.A. Urological anomalies in OHVIRA syndrome (Herlyn-Werner-Wunderlich syndrome). Urology Herald. 2022;10(2):109-123. (In Russ.) https://doi.org/10.21886/2308-6424-2022-10-2-109-123
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