urovestВестник урологииUrology Herald2308-6424Rostov State Medical University10.21886/2308-6424-2022-10-2-109-123urovest-552Research ArticleОБЗОРЫ ЛИТЕРАТУРЫREVIEWS ARTICLEУрологические аномалии при синдроме OHVIRA (Herlyn–Werner–Wunderlich синдром)Urological anomalies in OHVIRA syndrome (Herlyn-Werner-Wunderlich syndrome)https://orcid.org/0000-0002-9825-2809ЛодейкинаК.LodeikinaK.

Ксения Лодейкина – аспирант кафедры детской хирургии (с курсом детской урологии-андрологии); детский уролог-андролог

191015, г. Санкт-Петербург, ул. Кирочная, д.41

199053, г. Санкт-Петербург, Василеостровский район, 2-я линия, д. 47

Ksenia Lodeikina – M.D.; Postgrad. Student, Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course); Pediatric Urologist and Andrologist

41 Kirochnaya St., St. Petersburg, 191015

47 2nd Ln., Vasileostrovskiy district, St. Petersburg, 199053

ksenia.lod@gmail.comhttps://orcid.org/0000-0002-3957-1615КаганцовИ. М.KagantsovI. M.

Илья Маркович Каганцов – доктор медицинских наук; профессор кафедры детской хирургии; руководитель НИЛ хирургии врождённой и наследственной патологии

191015, г. Санкт-Петербург, ул. Кирочная, д.41

197341, г. Санкт-Петербург, ул. Аккуратова, д. 2

Ilya M. Kagantsov – M.D., Dr.Sci.(Med.); Prof., Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course); Head, Research Laboratory for Surgery of Congenital and Hereditary Pathology

41 Kirochnaya St., St. Petersburg, 191015

2 Akkuratova St., St. Petersburg, 197341

ilkagan@rambler.ruhttps://orcid.org/0000-0001-5884-9128КараваеваС. А.KaravaevaS. A.

Светлана Александровна Караваева – доктор медицинских наук, профессор; заведующая кафедрой детской хирургии

191015, г. Санкт-Петербург, ул. Кирочная, д.41

Svetlana A. Karavaeva – M.D., Dr.Sci.(Med.), Full Prof.; Head, Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course)

41 Kirochnaya St., St. Petersburg, 191015

swetl.karawaewa2015@yandex.ruhttps://orcid.org/0000-0002-0265-9728КохреидзеН. А.KokhreidzeN. A.

Надежда Анатольевна Кохреидзе – доктор медицинских наук; доцент кафедры детской гинекологии и женской репродуктологии; заведующая гинекологическим отделением для подростков

197341, г. Санкт-Петербург, ул. Аккуратова, д. 2

Nadezda A. Kokhreidze – M.D., Dr.Sci.(Med.); Assoc. Prof., Dept. of Pediatric Surgery (with the Pediatric Urology and Andrology Course); Head, Division of Adolescent Gynecology

2 Akkuratova St., St. Petersburg, 197341

kokhreidze@mail.ruФГБОУ ВО Северо-Западный государственный медицинский университет имени И.И. Мечникова Минздрава России; СПБ ГБУЗ «Детская городская больница №2 святой Марии Магдалины»РоссияMechnikov North-Western State Medical University; St. Mary Magdalene St. Petersburg Children's City Hospital No. 2Russian FederationФГБОУ ВО Северо-Западный государственный медицинский университет имени И.И. Мечникова Минздрава России; ФГБУ «Национальный медицинский исследовательский центр им. В.А. Алмазова» Минздрава РоссииРоссияMechnikov North-Western State Medical University; Almazov National Medical Research CentreRussian FederationФГБОУ ВО Северо-Западный государственный медицинский университет имени И.И. Мечникова Минздрава РоссииРоссияMechnikov North-Western State Medical UniversityRussian FederationФГБУ «Национальный медицинский исследовательский центр им. В.А. Алмазова» Минздрава РоссииРоссияAlmazov National Medical Research CentreRussian Federation202226062022102109123Copyright © Лодейкина К., Каганцов И.М., Караваева С.А., Кохреидзе Н.А., 20222022Лодейкина К., Каганцов И.М., Караваева С.А., Кохреидзе Н.А.Lodeikina K., Kagantsov I.M., Karavaeva S.A., Kokhreidze N.A.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.urovest.ru/jour/article/view/552

В работе приведён систематический обзор статей, касающихся синдрома OHVIRA (Herlyn–Werner–Wunderlich), найденных в PubMed/MedLine, Web of Science, Scopus, Scirus, The Cochrane Library и eLIBRARy, чтобы показать, как урологическая составляющая этого врождённого порока развития из сопутствующей аномалии стала важным диагностическим маркером. Рассмотрены различные попытки классификации данного состояния, усложнявшиеся по мере улучшения методов диагностики и обнаружения более сложных вариантов отклонений со стороны почки и мочеточника. Продемонстрировано, как за последние сто лет постепенно изменялось представление медицинского сообщества о синдроме OHVIRA, а возрастающий интерес детских урологов и хирургов в свою очередь способствовал ранней диагностике состояния и совершенствованию методов обследования.

We provide a systematic review of articles related to OHVIRA syndrome (Herlyn-Werner-Wunderlich syndrome), found in PubMed/MedLine, Web of Science, Scopus, Scirus, The Cochrane Library and eLIBRARy to show how the urological component of this congenital malformation, previously considered as a concomitant anomaly, has become an important diagnostic marker. Several attempts were made to classify this condition, and they got more complex to include these variants of abnormalities of the kidney and ureter that were found due to advances in imaging technology. As a result, the understanding of the medical community about the OHVIRA syndrome has gradually changed over the past hundred years, and the growing interest of pediatric urologists and surgeons, in turn, has contributed to the early diagnosis of the syndrome and the improvement of examination methods.

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The authors declare that there are no conflicts of interest present.